Paciente con notalgia parestésica y siringomielia: ¿relación o coincidencia? / A patient with notalgia paresthetica and syringomyelia: association or coincidence?

La notalgia parestésica (NP) es una neuropatía sensitiva comúnmente manifestada con prurito y aparición de una mácula hiperpigmentada a nivel del raquis dorsal en la mayoría de los casos. La fisiopatología de la NP es aún desconocida, aunque se considera su origen, por distintas causas, en una lesión producida en los nervios espinales. No existe un tratamiento definitivo para este desorden aunque son muchas las alternativas terapéuticas descritas. Presentamos el caso clínico de una paciente diagnosticada de NP y tratada satisfactoriamente con capsaicina, en quien encontramos una posible asociación etiológica con una siringomielia subclínica evidenciada en el estudio por resonancia magnética. Aunque teóricamente posible, no hemos encontrado otros artículos que asocien dichos cuadros (AU)

Notalgia paresthetica (NP) is a sensory neuropathy commonly manifested by pruritus and the appearance of a hyperpigmented macula, usually in the thoracic spine. The physiopathology of NP is unknown, although, for different reasons, its origin is considered to be an injury to the spinal nerves. There is no definitive treatment for this disorder, although many therapeutic alternatives have been used. We report the case of a patient diagnosed with notalgia paresthetica and successfully treated with capsaicin. In this patient, we found a possible etiological association with subclinical syringomyelia revealed by magnetic resonance imaging. Although this association is theoretically possible, we have found no other reports of an association between these two disorders (AU)

Tortícolis muscular congénita en fase de adulto / Congenital muscular torticollis in adults

La tortícolis muscular congénita (TMC) es una enfermedad frecuente, que debido a su fácil reconocimiento y exitoso tratamiento en los primeros meses de vida no suelen mostrar alteraciones clínicas en edades infantiles tardías o adultos. El escaso número de casos que prevalecen por encima de los primeros años de vida hace que exista una menor información sobre las decisiones terapéuticas a seguir. Básicamente se relegan, tras fracasar la fisioterapia, al uso de toxina botulínica o de una cirugía específica. Presentamos el caso clínico de una paciente diagnosticada finalmente, ya en edad adulta de TMC, y que fue tratada mediante sección unipolar de la porción clavicular del esternocleidomastoideo seguida de una rehabilitación específica, intensa y precoz, con muy buenos resultados estéticos y funcionales (AU)

Congenital muscular torticollis is a common condition. Because it is easy to recognize and its successful treatment during the first months of life, clinical changes are not usually found in the late childhood or adult age. As few cases prevail after the first years of life, there is less information about treatment decisions to follow. When physical therapy fails, these treatments are basically relegated to botulinum toxin or specific surgery. We report the case of a patient who was finally diagnosed in adulthood of congenital muscular torticollis. This patient was treated by unipolar sectioning of the clavicular portion of the sternocleidomastoid muscle. This was followed by specific, early and intense rehabilitation, with very good esthetic and functional results (AU)

Capsulitis adhesiva idiopática bilateral de cadera / Bilateral idiopathic adhesive capsulitis of the hip

La capsulitis adhesiva es una condición patológica de etiología desconocida en muchas ocasiones, caracterizada por la presencia de dolor y limitación de la movilidad. Esta alteración se produce con frecuencia en la articulación del hombro (frozen shoulder), aunque puede encontrarse en otras articulaciones. En la cadera es un cuadro infrecuente, normalmente relacionado con traumatismos locales. Presentamos el caso clínico de una mujer de 33 años con una capsulitis adhesiva bilateral e idiopática de caderas ya que no se encontró enfermedad reumatológica, hematológica, endocrina, tumoral o traumática que justificara su aparición. Debido a los problemas diagnósticos que se presentaron, y a pesar de realizar una rehabilitación intensa, posiblemente se planteó una indicación quirúrgica de forma tardía, por lo que se consiguieron unos resultados funcionales muy pobres. Se discute, a partir de la escasa literatura existente, diversos aspectos diagnósticos y terapéuticos de este proceso, comparándolo en ocasiones con la mayor información publicada en el caso del hombro

Adhesive capsulitis is a pathology of unknown ethiology, often characterized by the presence of pain and limited movility. It typically affects the shoulder joint (frozen shoulder), but can also affect other joints. Hip adhesive capsulitis is not very common and is usually associated with local traumatisms. We hereby present the clinical case of a 33 year old female with hip bilateral idiopatic adhesive capsulitis. No sign of illness (reumatological, haematological, endocrine, tumor or traumatism injury) that could cause the development of capsulitis was found. Due to the appearance of some problems during the diagnosis, and despite an intensive rehabilitation treatment, a late chirurgical intervention was carried out, showing poor functional improvement. Based on the sparse literature available, various diagnostical and therapeutical issues are discussed sometimes compared with the more numerous shoulder capsulitis reports

A multicentre study of the hospital care of 1500 patients with myelomeningocele.

The purpose of this paper is to describe the medical attention that is given to patients affected by myelomeningocele in Spain. We have used information extracted from the 'Multicentre study of patients suffering from spina bifida in Spain'. This material was collected between 1986 and 1988 from experiences with 1500 patients all over our country. 52.9% of the patients were male, and 47% female, and of the total number, 72.2% were under 15 years of age. Most of these patients attended public hospitals (78.5%) and on average each one had been admitted about seven times. The cost of hospitalisation of the sample has been assessed. Urology, orthopaedic surgery and rehabilitation are the specialties most involved. The most frequent complications were those related to the urinary system (66.1%).

Ambulation in patients with myelomeningocele: a study of 1500 patients.

Data from 1500 patients affected by spina bifida have been collected in a multicentre study in Spain from 1986 to 1988. This paper is concerned with a part of the data, specifically regarding the walking of patients and certain factors that influence the prognosis for ambulation. The neurological level of lesion most commonly present was lumbosacral (65.6%). Hydrocephalus was frequent (62% of the sample), and has significant implications regarding prognosis for walking. Hip dislocation (32%) and scoliosis (22.9%) were orthopaedic problems noted in our sample. Pressure sores appeared in 31.7% of the patients. The onset of walking ability has been studied; 15% of the sample started walking at an age older than 5 years. Finally, different modalities of ambulation are described according to the use of ancillary devices, and in independence in activities of daily living.